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Search / Trial NCT01668186

Longitudinal Natural History Study of Patients With Peroxisome Biogenesis Disorders (PBD)

Launched by MCGILL UNIVERSITY HEALTH CENTRE/RESEARCH INSTITUTE OF THE MCGILL UNIVERSITY HEALTH CENTRE · Aug 14, 2012

Trial Information

Current as of June 28, 2025

Recruiting

Keywords

Peroxisome Biogenesis Disorders Pbd Zellweger Spectrum Disorder Rhizomelic Chondrodysplasia Punctata Dbp Acox1 Amacr Ard Acbd5 Zsd Rcdp Acox2 Abcd3 Adult Refsum Phyh Sc Px Rcdp1 Rcdp2 Rcdp3

ClinConnect Summary

This clinical trial is studying a group of inherited disorders called Peroxisome Biogenesis Disorders (PBD), which affect how certain cell structures, called peroxisomes, are formed and function. These disorders can lead to various developmental and metabolic issues, but researchers are still working to fully understand them. The goal of this study is to gather more information about patients with PBD by following their health over time. The study will collect data from medical evaluations, blood tests, urine tests, and imaging studies, both from patients who can visit the clinic and those who cannot. This information will help researchers establish better care standards and improve how these conditions are managed.

To be eligible for this study, participants must have a diagnosed PBD or a similar condition caused by a single enzyme or protein defect. Anyone interested in participating will need to provide their medical records and, if possible, join the study for up to five years. The research team aims to create a comprehensive database of information to better understand these disorders and ultimately help improve treatment options for those affected.

Gender

ALL

Eligibility criteria

  • Inclusion Criteria:
  • Diagnosis of PBD or
  • Single peroxisome enzyme/protein defect with phenotype similar to PBD
  • Exclusion Criteria:
  • Not a PBD
  • Not a single peroxisome enzyme/protein defect with phenotype similar to PBD

About Mcgill University Health Centre/Research Institute Of The Mcgill University Health Centre

The McGill University Health Centre (MUHC) and the Research Institute of the McGill University Health Centre (RI-MUHC) are leading institutions in clinical research and healthcare innovation. With a commitment to advancing medical knowledge and improving patient outcomes, the MUHC integrates cutting-edge research with high-quality patient care. The RI-MUHC fosters a collaborative environment where multidisciplinary teams engage in transformative research across various fields, including oncology, neurology, and cardiovascular health. By leveraging state-of-the-art facilities and a robust network of clinical expertise, both entities strive to translate scientific discoveries into effective treatments, ultimately enhancing the quality of life for patients locally and globally.

Locations

Montreal, Quebec, Canada

Patients applied

0 patients applied

Trial Officials

Nancy E Braverman, MD, MS

Principal Investigator

McGill University Health Center, Montreal Childrens Hopital

Timeline

First submit

Trial launched

Trial updated

Estimated completion

Not reported

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