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Search / Trial NCT04905693

Extension Study of Inhaled Treprostinil in Subjects With Idiopathic Pulmonary Fibrosis

Launched by UNITED THERAPEUTICS · May 25, 2021

Trial Information

Current as of July 22, 2025

Enrolling by invitation

Keywords

Treprostinil Ipf Ild

ClinConnect Summary

Study RIN-PF-302 is a Phase 3, multicenter, open-label extension (OLE) study for eligible subjects who completed Study RIN-PF-301 or Study RIN-PF-303 to evaluate the long-term safety and tolerability of inhaled treprostinil in subjects with idiopathic pulmonary fibrosis (IPF). Following OLE entry, subjects will return at Week 4, Week 12, and every 12 weeks thereafter for up to 6 years or until the subject prematurely discontinues study treatment due an adverse event (AE)/serious adverse event (SAE) or other reason, inhaled treprostinil becomes commercially available for IPF, or the study is...

Gender

ALL

Eligibility criteria

  • Inclusion Criteria:
  • 1. Subject gives voluntary informed consent to participate in the study.
  • 2. The subject participated in Study RIN-PF-301 or Study RIN-PF-303 and remained on study drug and completed all scheduled study visits or was enrolled in Study RIN-PF-301 or Study RIN-PF-303 at the time that the study or study subject was discontinued by the Sponsor.
  • 3. Women of childbearing potential must be non-pregnant (as confirmed by a urine pregnancy test at OLE Entry Visit and Baseline) and non-lactating, and will abstain from intercourse (when it is in line with their preferred and usual lifestyle) or use 2 medically acceptable, highly effective forms of contraception for the duration of the study, and at least 30 days after discontinuing study drug.
  • 4. Males with a partner of childbearing potential must use a condom for the duration of treatment and for at least 48 hours after discontinuing study drug.
  • 5. In the opinion of the Investigator, the subject is able to communicate effectively with study personnel, and is considered reliable, willing, and likely to be cooperative with protocol requirements, including attending all study visits.
  • Exclusion Criteria:
  • 1. Subject is pregnant or lactating.
  • 2. In the opinion of the Investigator, enrollment in Study RIN-PF-302 would represent a risk to the subject's overall health.

About United Therapeutics

United Therapeutics is a leading biotechnology company dedicated to addressing the unmet medical needs of patients with life-threatening conditions, particularly in the fields of pulmonary arterial hypertension and organ transplantation. Founded in 1996, the company focuses on the development and commercialization of innovative therapies that enhance patient quality of life and extend survival. With a robust pipeline and a commitment to scientific excellence, United Therapeutics partners with healthcare providers, researchers, and advocacy groups to drive advancements in treatment options and improve outcomes for patients worldwide.

Locations

Philadelphia, Pennsylvania, United States

Kansas City, Kansas, United States

Minneapolis, Minnesota, United States

Houston, Texas, United States

Milwaukee, Wisconsin, United States

Charleston, South Carolina, United States

Boston, Massachusetts, United States

Bronx, New York, United States

Saint Louis, Missouri, United States

Brussels, , Belgium

Maywood, Illinois, United States

Chicago, Illinois, United States

Detroit, Michigan, United States

Rochester, New York, United States

Oklahoma City, Oklahoma, United States

Dallas, Texas, United States

Malaga, , Spain

New Orleans, Louisiana, United States

Stanford, California, United States

Philadelphia, Pennsylvania, United States

Atlanta, Georgia, United States

Barcelona, , Spain

Santander, , Spain

Houston, Texas, United States

Boston, Massachusetts, United States

Cleveland, Ohio, United States

Falls Church, Virginia, United States

Nashville, Tennessee, United States

Jacksonville, Florida, United States

Tucson, Arizona, United States

Los Angeles, California, United States

Weston, Florida, United States

Gainesville, Florida, United States

Madrid, , Spain

Boston, Massachusetts, United States

Greenville, North Carolina, United States

Madrid, , Spain

Jacksonville, Florida, United States

Westmead, , Australia

Hamilton, Ontario, Canada

Granada, , Spain

Ashkelon, , Israel

Rennes, , France

Birmingham, Alabama, United States

Albuquerque, New Mexico, United States

Liège, , Belgium

Baltimore, Maryland, United States

Haifa, , Israel

Kfar Saba, , Israel

Leuven, , Belgium

Jerusalem, , Israel

Denver, Colorado, United States

Chermside, Queensland, Australia

Seoul, , Korea, Republic Of

Barcelona, , Spain

Madrid, , Spain

Antwerpen, , Belgium

Portland, Oregon, United States

Cincinnati, Ohio, United States

Camperdown, , Australia

Liège, , Belgium

Taipei, , Taiwan

L´Hospitalet De Llobregat, Barcelona, Spain

Louisville, Kentucky, United States

Orlando, Florida, United States

Shreveport, Louisiana, United States

Murray, Utah, United States

New Taipei City, , Taiwan

Roma, , Italy

Melbourne, Victoria, Australia

Columbus, Ohio, United States

Amiens, , France

Palm Springs, California, United States

Chesterfield, Missouri, United States

Santiago De Compostela, , Spain

Rock Hill, South Carolina, United States

Oviedo, Asturias, Spain

Trois Rivières, Quebec, Canada

The Woodlands, Texas, United States

Macquarie Park, New South Wales, Australia

Yvoir, Namur, Belgium

Indianapolis, Indiana, United States

Gainesville, Florida, United States

Kaohsiung, , Taiwan

Winston Salem, North Carolina, United States

New Hyde Park, New York, United States

Charlottesville, Virginia, United States

Macquarie University, New South Wales, Australia

Dallas, Texas, United States

Seongnam Si, Gyeonggido, Korea, Republic Of

Murcia, , Spain

Greensboro, North Carolina, United States

Incheon, , Korea, Republic Of

South Brisbane, Queensland, Australia

Phoenix, Arizona, United States

Ciudad Autónoma De Buenos Aires, , Argentina

Cleveland, Ohio, United States

Québec, , Canada

Modena, Emilia Romagna, Italy

Louisville, Kentucky, United States

Palma De Mallorca, Baleares, Spain

Hamilton, Waikato, New Zealand

Madison, Wisconsin, United States

Richmond, Virginia, United States

Salt Lake City, Utah, United States

Jacksonville, Florida, United States

Tampa, Florida, United States

Forlì, , Italy

Columbia, South Carolina, United States

Antwerpen, , Belgium

Chermside, Queensland, Australia

Kissimmee, Florida, United States

Rochester, Minnesota, United States

Omaha, Nebraska, United States

Knoxville, Tennessee, United States

Monterrey, Nuevo León, Mexico

Lima, , Peru

Phoenix, Arizona, United States

Newport Beach, California, United States

Saint Petersburg, Florida, United States

Anderlecht, Brussels, Belgium

Tours, Indre Et Loire, France

Mckinney, Texas, United States

Franklin, Arizona, United States

Malaga, Málaga, Spain

Aarhus N, , Denmark

Seongnam Si, Gyeonggido, Korea, Republic Of

Ramat Gan, Tel Aviv, Israel

Jerusalem, Yerushalayim, Israel

Mar Del Plata, Buenos Aires, Argentina

Rehovot, Hamerkaz, Israel

Mcallen, Texas, United States

Ancona, , Italy

Roma, Lazio, Italy

Jackson, Mississippi, United States

Sacramento, California, United States

Ann Arbor, Michigan, United States

Atlanta, Georgia, United States

Talca, Maule, Chile

Quillota, Valparaiso, Chile

Petah Tiqva, , Israel

Seoul, Seoul Teugbyeolsi, Korea, Republic Of

Kaohsiung, , Taiwan

Tel Aviv, , Israel

Rosenheim, Bayern, Germany

Dongjak Gu, Seoul Teugbyeolsi, Korea, Republic Of

Ajax, Ontario, Canada

Ciudad Autónoma De Buenos Aires, Buenos Aires, Argentina

Córdoba, , Argentina

Mendoza, , Argentina

Santiago, Metropolitana, Chile

Santiago, Región Metropolitana, Chile

Hellerup, , Denmark

Odense C, , Denmark

Bron, , France

Silver Spring, Maryland, United States

Rio Cuarto, , Argentina

Marseille, Bouches Du Rhône, France

Toulouse, Haute Garonne, France

Paris, , France

Siena, Toscana, Italy

Hadera, Haifa, Israel

Rotterdam, Zuid Holland, Netherlands

Royal Oak, Michigan, United States

Hershey, Pennsylvania, United States

Philadelphia, Pennsylvania, United States

Bobigny, , France

Reims, , France

Catania, Sicilia, Italy

Seoul, Seoul Teugbyeolsi, Korea, Republic Of

Christchurch, , New Zealand

Ciudad De Mexico, , Mexico

Antwerpen, , Belgium

Monterrey, Nuevo León, Mexico

Paris, , France

Milan, Lombardia, Italy

Heerlen, Limburg, Netherlands

Córdoba, , Argentina

San Miguel De Tucumán, Tucumán, Argentina

San Miguel De Tucumán, Tucumán, Argentina

Lima, , Peru

Trois Rivières, Quebec, Canada

Santiago, Región Metropolitana, Chile

Aalst, , Belgium

Ajax, Ontario, Canada

Caen, Calvados, France

Rouen, Seine Maritime, France

Löwenstein, Baden Württemberg, Germany

München, Bayern, Germany

Essen, Nordrhein Westfalen, Germany

Coswig, Sachsen, Germany

Bad Berka, Thüringen, Germany

Cusco, , Peru

Santiago De Compostela, A Coruña, Spain

Incheon, Incheon Gwang'yeogsi, Korea, Republic Of

Rio Cuarto, , Argentina

Mendoza, Provincia De Mendoza, Argentina

San Miguel De Tucumán, , Argentina

San Miguel De Tucumán, , Argentina

Santiago, , Chile

Santiago, , Chile

Marseille, , France

Löwenstein, , Germany

Bad Berka, , Germany

Monterrey, , Mexico

Monterrey, , Mexico

Rosario, Provincia De Santa Fe, Argentina

Cairns, Queensland, Australia

Patients applied

0 patients applied

Timeline

First submit

Trial launched

Trial updated

Estimated completion

Not reported

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