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Search / Trial NCT05312879

Phase 2/3 Adaptive Study of VX-147 in Adult and Pediatric Participants With APOL1- Mediated Proteinuric Kidney Disease

Launched by VERTEX PHARMACEUTICALS INCORPORATED · Mar 28, 2022

Trial Information

Current as of June 27, 2025

Recruiting

Keywords

Apol1 Mediated Kidney Disease (Amkd)

ClinConnect Summary

This clinical trial is studying a new treatment called VX-147 for patients with a specific type of kidney disease known as APOL1-mediated proteinuric kidney disease. This condition can lead to protein in the urine, which indicates that the kidneys are not working properly. The trial aims to find out if VX-147 is effective and safe for both adults and children who have this type of kidney disease.

To participate in the trial, individuals must have a certain genetic makeup (APOL1 genotype) and be diagnosed with proteinuric kidney disease. However, those who have had a solid organ or bone marrow transplant, have uncontrolled high blood pressure, or a history of diabetes may not be eligible. Participants can expect to receive the study drug and will be closely monitored throughout the trial to ensure their safety and to see how well the treatment works. This study is currently recruiting participants, and it is open to people of all genders between the ages of 1 and 65 years.

Gender

ALL

Eligibility criteria

  • Key Inclusion Criteria:
  • APOL1 genotype of G1/G1, G2/G2, or G1/G2
  • Proteinuric kidney disease
  • Key Exclusion Criteria:
  • Solid organ or bone marrow transplant
  • Uncontrolled hypertension
  • History of diabetes mellitus
  • Known underlying cause of kidney disease including but not limited to sickle cell disease
  • Other protocol defined Inclusion/Exclusion criteria apply.

About Vertex Pharmaceuticals Incorporated

Vertex Pharmaceuticals Incorporated is a global biotechnology company dedicated to the innovation and development of transformative therapies for serious diseases, particularly those with significant unmet medical needs. Founded in 1989 and headquartered in Boston, Massachusetts, Vertex specializes in the research and commercialization of treatments for cystic fibrosis and other genetic disorders. Leveraging cutting-edge science and a commitment to patient-centric solutions, Vertex collaborates with healthcare professionals and researchers to advance clinical trials and bring groundbreaking therapies to market, aiming to improve the lives of patients worldwide.

Locations

Chicago, Illinois, United States

Kansas City, Kansas, United States

Milwaukee, Wisconsin, United States

Charleston, South Carolina, United States

Chicago, Illinois, United States

Bronx, New York, United States

Iowa City, Iowa, United States

London, , United Kingdom

Boston, Massachusetts, United States

New Orleans, Louisiana, United States

Detroit, Michigan, United States

Los Angeles, California, United States

Little Rock, Arkansas, United States

Boston, Massachusetts, United States

Hackensack, New Jersey, United States

Philadelphia, Pennsylvania, United States

Baltimore, Maryland, United States

Barcelona, , Spain

Indianapolis, Indiana, United States

Boston, Massachusetts, United States

Birmingham, Alabama, United States

Cleveland, Ohio, United States

Seattle, Washington, United States

Gainesville, Florida, United States

Richmond, Virginia, United States

Baltimore, Maryland, United States

Pittsburgh, Pennsylvania, United States

Fort Worth, Texas, United States

Cincinnati, Ohio, United States

Dallas, Texas, United States

Philadelphia, Pennsylvania, United States

Brooklyn, New York, United States

Lubbock, Texas, United States

New York, New York, United States

New Haven, Connecticut, United States

Nashville, Tennessee, United States

Birmingham, Alabama, United States

San Francisco, California, United States

Hines, Illinois, United States

Barcelona, , Spain

Jackson, Mississippi, United States

New York, New York, United States

São Paulo, , Brazil

Ibadan, , Nigeria

Columbus, Ohio, United States

Seattle, Washington, United States

Amsterdam, , Netherlands

Albuquerque, New Mexico, United States

Columbus, Mississippi, United States

Olive Branch, Mississippi, United States

Brandon, Florida, United States

Oxon Hill, Maryland, United States

Leuven, , Belgium

Torrance, California, United States

Manchester, , United Kingdom

Sao Paulo, , Brazil

Seville, , Spain

Houston, Texas, United States

Middlebury, Connecticut, United States

Lansing, Michigan, United States

Cleveland, Ohio, United States

Huntsville, Alabama, United States

Madrid, , Spain

Nottingham, , United Kingdom

Chattanooga, Tennessee, United States

Porto Alegre, , Brazil

Charleston, South Carolina, United States

Bronx, New York, United States

Barcelona, , Spain

Paris, , France

London, , United Kingdom

Metairie, Louisiana, United States

Tupelo, Mississippi, United States

Chapel Hill, North Carolina, United States

Brooklyn, New York, United States

Columbia, South Carolina, United States

Farmington Hills, Michigan, United States

Baton Rouge, Louisiana, United States

Los Angeles, California, United States

Newark, New Jersey, United States

Rio De Janeiro, , Brazil

Granada Hills, California, United States

Lauderdale Lakes, Florida, United States

Atlanta, Georgia, United States

Los Angeles, California, United States

Hialeah, Florida, United States

Washington, District Of Columbia, United States

Arlington, Texas, United States

Gainesville, Florida, United States

Kumasi, , Ghana

Albuquerque, New Mexico, United States

Roseville, Michigan, United States

Sacramento, California, United States

Créteil, , France

Bradenton, Florida, United States

São José Do Rio Preto, , Brazil

Cali, , Colombia

Laurelton, New York, United States

London, , United Kingdom

Saint Louis, Missouri, United States

Springfield, Massachusetts, United States

San Antonio, Texas, United States

Huntsville, Alabama, United States

Medellín, , Colombia

Miami, Florida, United States

Manchester, , United Kingdom

Dallas, Texas, United States

Enugu, , Nigeria

Dallas, Texas, United States

New Orleans, Louisiana, United States

Córdoba, , Spain

Leuven, , Belgium

Lawrenceville, Georgia, United States

Minneapolis, Minnesota, United States

New Orleans, Louisiana, United States

Columbus, Georgia, United States

Webster, Texas, United States

London, , United Kingdom

Belo Horizonte, , Brazil

Camden, New Jersey, United States

Ikeja, , Nigeria

Wauwatosa, Wisconsin, United States

Tyrone, Georgia, United States

Miami, Florida, United States

Bronx, New York, United States

Flint, Michigan, United States

Charlotte, North Carolina, United States

Decatur, Georgia, United States

San Juan, , Puerto Rico

Nashville, Tennessee, United States

Natchitoches, Louisiana, United States

New York, New York, United States

Shreveport, Louisiana, United States

Tampa, Florida, United States

Houston, Texas, United States

East Providence, Rhode Island, United States

Brunswick, Georgia, United States

Birmingham, Alabama, United States

Washington, District Of Columbia, United States

Atlanta, Georgia, United States

Las Vegas, Nevada, United States

Paris, , France

Paris, , France

Paris, , France

Leicester, , United Kingdom

Southwark, , United Kingdom

Union City, Georgia, United States

Delray Beach, Florida, United States

Miami, Florida, United States

Temple Terrace, Florida, United States

Granada Hills, California, United States

Lisboa, , Portugal

Orange, California, United States

Orlando, Florida, United States

Bronx, New York, United States

Victorville, California, United States

Edina, Minnesota, United States

Little Rock, Arkansas, United States

Mesa, Arizona, United States

Coral Gables, Florida, United States

Hollywood, Florida, United States

Atlanta, Georgia, United States

Roseville, Minnesota, United States

Flushing, New York, United States

Laurelton, New York, United States

Greenville, North Carolina, United States

Jacksonville, North Carolina, United States

Kinston, North Carolina, United States

New Bern, North Carolina, United States

Wilmington, North Carolina, United States

Winston Salem, North Carolina, United States

Virginia Beach, Virginia, United States

Dallas, Texas, United States

Loures, , Portugal

Phoenix, Arizona, United States

Fresno, California, United States

Cape Coral, Florida, United States

Shreveport, Louisiana, United States

Chapel Hill, North Carolina, United States

Miami Springs, Florida, United States

Nashville, Tennessee, United States

London, , United Kingdom

Spartanburg, South Carolina, United States

Bloomfield, Connecticut, United States

Coral Springs, Florida, United States

Sanford, Florida, United States

Las Vegas, Nevada, United States

Bronx, New York, United States

El Paso, Texas, United States

Houston, Texas, United States

Shenandoah, Texas, United States

Norfolk, Virginia, United States

Montreal, , Canada

Grenoble, , France

Mishawaka, Indiana, United States

Cary, North Carolina, United States

San Antonio, Texas, United States

Grenoble, , France

Le Kremlin Bicêtre, , France

Saint Ouen, , France

Santo Andre, , Brazil

Savannah, Georgia, United States

Norfolk, Virginia, United States

Marseille, , France

Los Angeles, California, United States

New York, New York, United States

Limoges, , France

Mansfield, Texas, United States

Houston, Texas, United States

Toulouse, , France

Carshalton, , United Kingdom

Atlanta, Georgia, United States

The Woodlands, Texas, United States

London, , United Kingdom

Bay Pines, Florida, United States

Woluwe Saint Lambert, Brussels, Belgium

Phoenix, Arizona, United States

Augusta, Georgia, United States

Philadelphia, Pennsylvania, United States

Dallas, Texas, United States

Columbus, Georgia, United States

Grenada, Mississippi, United States

Houston, Texas, United States

Hallandale Beach, Florida, United States

Minas Gerais, , Brazil

São Paulo, , Brazil

Amadora, , Portugal

Toronto, , Canada

West Springfield, Massachusetts, United States

Great Neck, New York, United States

Atlanta, Georgia, United States

Saint Louis, Missouri, United States

New York, New York, United States

Ribeirão Preto, , Brazil

Birmingham, , United Kingdom

Fayetteville, Georgia, United States

Charlottesville, Virginia, United States

Curitiba, , Brazil

Curitiba, , Brazil

Juiz De Fora, , Brazil

Juiz De Fora, , Brazil

Rio De Janeiro, , Brazil

London, , United Kingdom

Goiania, , Brazil

Salvador, , Brazil

Silver Spring, Maryland, United States

Coral Gables, Florida, United States

Annapolis, Maryland, United States

Dallas, Texas, United States

Dallas, Texas, United States

Porto Alegre, , Brazil

Rio De Janeiro, , Brazil

Roxbury, Massachusetts, United States

Overland Park, Kansas, United States

Arlington, Texas, United States

Richmond, Virginia, United States

Fortaleza, , Brazil

Juiz De Fora, , Brazil

Ribeirao Preto, , Brazil

Brandon, Florida, United States

Evergreen Park, Illinois, United States

Palos Hills, Illinois, United States

Ann Arbor, Michigan, United States

Dallas, Texas, United States

East Point, Georgia, United States

Saint Clair Shores, Michigan, United States

Saint Louis, Missouri, United States

Las Vegas, Nevada, United States

Durham, North Carolina, United States

Salvador, , Brazil

Atlántico, , Colombia

New Orleans, Louisiana, United States

Gaithersburg, Maryland, United States

Accra, , Ghana

Birmingham, , United Kingdom

Atlanta, Georgia, United States

Cartagena, , Colombia

Rio Piedras, , Puerto Rico

Tampa, Florida, United States

Orlando, Florida, United States

New York, New York, United States

Bogota, , Colombia

Lewisville, Texas, United States

Fortaleza, , Brazil

Saint Louis, Missouri, United States

Norfolk, Virginia, United States

Norfolk, Virginia, United States

Atlántico, , Colombia

Fayette, Mississippi, United States

Lisboa, , Portugal

Ridgeland, Mississippi, United States

Sanford, Florida, United States

West Monroe, Louisiana, United States

Fairhope, Alabama, United States

Cantonments, , Ghana

Vestavia Hills, Alabama, United States

Chicago, Illinois, United States

Montgomery, Alabama, United States

Charleston, South Carolina, United States

Memphis, Tennessee, United States

Campinas, , Brazil

Marilia, , Brazil

Guadeloupe, , France

Alabaster, Alabama, United States

College Park, Georgia, United States

Fort Wayne, Indiana, United States

Brooklyn, New York, United States

Cincinnati, Ohio, United States

Cleveland, Ohio, United States

Basildon, , United Kingdom

Recife, , Brazil

Nottingham, Maryland, United States

Edina, Minnesota, United States

Dallas, Texas, United States

Aracaju, , Brazil

Meireles, , Brazil

Sao Paulo, , Brazil

Agodi, Ibadan, , Nigeria

Botucatu, , Brazil

Botucatu, , Brazil

Yaba, , Nigeria

Chicago, Illinois, United States

New York, New York, United States

Salvador, , Brazil

Medellin, , Colombia

Nottingham, , United Kingdom

Jacksonville, Florida, United States

Acworth, Georgia, United States

Douglasville, Georgia, United States

Memphis, Tennessee, United States

Dallas, Texas, United States

Ibague, , Colombia

Idi Araba, , Nigeria

Birmingham, , United Kingdom

Manchester, , United Kingdom

Bellshill, , United Kingdom

Orlando, Florida, United States

Lewisville, Texas, United States

Birmingham, Alabama, United States

Hamilton, New Jersey, United States

Mesa, Arizona, United States

Augusta, Georgia, United States

Bronx, New York, United States

Houston, Texas, United States

Agodi, , Nigeria

Atlanta, Georgia, United States

Augusta, Georgia, United States

Miami, Florida, United States

Orlando, Florida, United States

Chicago, Illinois, United States

Baltimore, Maryland, United States

Wauwatosa, Wisconsin, United States

Fortaleza, , Brazil

Pointe à Pitre Cedex, , France

Mayaguez, , Puerto Rico

Orlando, Florida, United States

Saint Louis, Missouri, United States

Orlando, Florida, United States

Patients applied

0 patients applied

Timeline

First submit

Trial launched

Trial updated

Estimated completion

Not reported

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